Now showing items 1-2 of 2

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      Beneficial effect of ursodeoxycholic acid in patients with acyl-CoA oxidase 2 (ACOX2) deficiency-associated hypertransaminasemia 

      Alonso Peña, Marta; Espinosa Escudero, Ricardo; Herráez Aguilar, Elisa; Briz Sánchez, Oscar; Cagigal, María Luisa; González Santiago, Jesús M.; Ortega Alonso, Aida; Fernández Rodríguez, Conrado; Bujanda Fernández de Pierola, Luis ORCID; Calvo Sánchez, Marta; D'Avola, Delia; Londono, Maria Carlota; Diago, Moisés; Fernández Checa, José Carlos; García Ruiz, Carmen; Andrade, Raúl; Lammert, Frank; Prieto, Jesús; Crespo, Javier; Juanpérez, Javier; Díaz González, Álvaro; Monte, María J.; García Marín, Jose Juan (Wiley, 2022-11)
      Background and Aims: A variant (p.Arg225Trp) of peroxisomal acyl-CoA oxidase 2 (ACOX2), involved in bile acid (BA) side-chain shortening, has been associated with unexplained persistent hypertransaminasemia and ...
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      TREM-2 plays a protective role in cholestasis by acting as a negative regulator of inflammation 

      Labiano Ciriza, Ibone; Agirre Lizaso, Aloña; Olaizola Rebe, Paula; Echebarria, Anne; Huici Izagirre, Maider; Olaizola, Irene; Esparza Baquer, Aitor ORCID; Sharif, Omar; Hijona Muruamendiaraz, Elizabeth; Milkiewicz, Piotr; Milkiewicz, Malgorzata; González Romero, Francisco; Aspichueta Celaá, Patricia; Monte, María J.; García Marín, Jose Juan; Vucur, Michael; Luedde, Tom; Marzioni, Marco; Mann, Derek A.; Bujanda Fernández de Pierola, Luis ORCID; Perugorria Montiel, María Jesús (Elsevier, 2022-10)
      Background & Aims: Inflammation, particularly that mediated by bacterial components translocating from the gut to the liver and binding to toll-like receptors (TLRs), is central to cholestatic liver injury. The triggering ...