Browsing Artículos, Comunicaciones, Libros by Author "Caballero Camino, Francisco Javier"
Now showing items 1-4 of 4
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Inhibition of NAE-dependent protein hyper-NEDDylation in cystic cholangiocytes halts cystogenesis in experimental models of polycystic liver disease
Lee-Law, Pui Y.; Olaizola Rebe, Paula; Caballero Camino, Francisco Javier; Izquierdo Sánchez, Laura; Rodrigues, Pedro M.; Perugorria Montiel, María Jesús; Azkargorta, Mikel; Elortza, Felix; Martínez Chantar, María Luz
; Aspichueta Celaá, Patricia; Bujanda Fernández de Pierola, Luis
; Drenth, Joost P. H.; Bañales Asurmendi, Jesús María
(Sage, 2021-09)
Background Polycystic liver diseases (PLDs) are genetic inherited disorders characterized by the progressive growth of numerous intrahepatic biliary cysts, which are the main cause of morbidity. Previous studies revealed ... -
Synthetic Conjugates of Ursodeoxycholic Acid Inhibit Cystogenesis in Experimental Models of Polycystic Liver Disease
Caballero Camino, Francisco Javier; Rivilla de la Cruz, Iván
; Herráez Aguilar, Elisa; Briz Sánchez, Oscar; Santos Laso, Álvaro; Izquierdo Sánchez, Laura; Lee-Law, Pui Y.; Rodrigues, Pedro M.; Muñoz Garrido, Patricia; Jin, Sujeong; Peixoto, Estanislao; Richard, Seth; Gradilone, Sergio A.; Perugorria Montiel, María Jesús; Esteller, Manel; Bujanda Fernández de Pierola, Luis
; Marin, José J. G.; Bañales Asurmendi, Jesús María
; Cossío Mora, Fernando Pedro
(Wiley, 2020-09-22)
Background and Aims Polycystic liver diseases (PLDs) are genetic disorders characterized by progressive development of symptomatic biliary cysts. Current surgical and pharmacological approaches are ineffective, and liver ... -
Targeting NAE1-mediated protein hyper-NEDDylation halts cholangiocarcinogenesis and impacts on tumor-stroma crosstalk in experimental models.
Olaizola Rebe, Paula; Lee-Law, Pui Y.; García Fernández de Barrena, Maite; Álvarez Asiain, Laura; Cadamuro, Massimiliano; Azkargorta, Mikel; O’Rourke, Colm J.; Caballero Camino, Francisco Javier
; Olaizola, Irene; Rodríguez Macías, Rocío Isabel; García Marín, Jose Juan; Serrano Maciá, Marina; Martínez Chantar, María Luz
; Ávila, Matías A.
; Aspichueta Celaá, Patricia; CALVISI, Diego Francesco
; Evert, Matthias; Fabris, Luca; Castro, Rui
; Elortza, Felix; Andersen, Jesper B.; Bujanda Fernández de Pierola, Luis
; Rodrigues, Pedro M.; Perugorria, Maria Jesus
; Bañales Asurmendi, Jesús María
(Elsevier, 2022-07)
[EN] BACKGROUND & AIMS: Cholangiocarcinoma (CCA) comprises a heterogeneous group of malignant tumors associated with dismal prognosis. Alterations in post-translational modifications (PTMs), including NEDDylation, result ... -
Targeting UBC9-Mediated Protein Hyper-SUMOylation in Cystic Cholangiocytes Halts Polycystic Liver Disease in Experimental Models
Lee-Law, Pui Y.; Olaizola Rebe, Paula; Caballero Camino, Francisco Javier; Izquierdo Sánchez, Laura; Rodrigues, Pedro M.; Santos Laso, Álvaro; Azkargorta, Mikel; Elortza, Felix; Martínez Chantar, María Luz
; Perugorria Montiel, María Jesús; Aspichueta Celaá, Patricia; Marzioni, Marco; LaRusso, Nicholas F.; Bujanda Fernández de Pierola, Luis
; Drenth, Joost P. H.; Bañales Asurmendi, Jesús María
(Elsevier, 2021-02)
BACKGROUND & AIMS: Polycystic liver diseases (PLDs) are genetic disorders characterized by progressive development of multiple fluid-filled biliary cysts. Most PLD-causative genes participate in protein biogenesis and/or ...